IgG4-related aortitis
MONDO:0018672Mondo
Findings
No curated finding names IgG4-related aortitis yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Features
25 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Increased circulating IgG4 concentrationHPOHP:0032300
- Very frequent (80% to 99% of cases)
- Increased circulating immunoglobulin concentrationHPOHP:0010702
- Very frequent (80% to 99% of cases)
- Abdominal painHPOHP:0002027
- Frequent (30% to 79% of cases)
- AllergyHPOHP:0012393
- Frequent (30% to 79% of cases)
- Antinuclear antibody positivityHPOHP:0003493
- Frequent (30% to 79% of cases)
- AsthmaHPOHP:0002099
- Frequent (30% to 79% of cases)
- AutoimmunityHPOHP:0002960
- Frequent (30% to 79% of cases)
- Elevated circulating C-reactive protein concentrationHPOHP:0011227
- Frequent (30% to 79% of cases)
- Elevated erythrocyte sedimentation rateHPOHP:0003565
- Frequent (30% to 79% of cases)
- FeverHPOHP:0001945
- Frequent (30% to 79% of cases)
- Increased circulating IgE concentrationHPOHP:0003212
- Frequent (30% to 79% of cases)
- Increased inflammatory responseHPOHP:0012649
- Frequent (30% to 79% of cases)
Show the remaining 13
- Low back painHPOHP:0003419
- Frequent (30% to 79% of cases)
- Severely increased total eosinophil countHPOHP:0032061
- Frequent (30% to 79% of cases)
- Thoracic aortic aneurysmHPOHP:0012727
- Frequent (30% to 79% of cases)
- Weight lossHPOHP:0001824
- Frequent (30% to 79% of cases)
- Abnormal aortic arch morphologyHPOHP:0012303
- Occasional (5% to 29% of cases)
- Abnormal common carotid artery morphologyHPOHP:0430021
- Occasional (5% to 29% of cases)
Where it sits
Other names
1 name
Resolves to: IgG4-related aortitis
- Also called
- IgG4-related periaortitis