IgA pemphigus
MONDO:0034127Mondo
Findings
No curated finding names IgA pemphigus yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Features
19 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Abnormal blistering of the skinHPOHP:0008066
- Very frequent (80% to 99% of cases)
- Neutrophilic infiltration of the skinHPOHP:0031234
- Very frequent (80% to 99% of cases)
- Skin vesicleHPOHP:0200037
- Very frequent (80% to 99% of cases)
- AcantholysisHPOHP:0100792
- Frequent (30% to 79% of cases)
- Autoimmune antibody positivityHPOHP:0030057
- Frequent (30% to 79% of cases)
- Generalized abnormality of skinHPOHP:0011354
- Frequent (30% to 79% of cases)
- Linear IgA deposits along the epidermal basement membrane zoneHPOHP:0031539
- Frequent (30% to 79% of cases)
- Oral mucosal blistersHPOHP:0200097
- Frequent (30% to 79% of cases)
- PainHPOHP:0012531
- Frequent (30% to 79% of cases)
- PruritusHPOHP:0000989
- Frequent (30% to 79% of cases)
- PustuleHPOHP:0200039
- Frequent (30% to 79% of cases)
- Skin erosionHPOHP:0200041
- Frequent (30% to 79% of cases)
Show the remaining 7
- Skin plaqueHPOHP:0200035
- Frequent (30% to 79% of cases)
- Annular cutaneous lesionHPOHP:0025528
- Occasional (5% to 29% of cases)
- Cutaneous abscessHPOHP:0031292
- Occasional (5% to 29% of cases)
- Increased circulating IgA concentrationHPOHP:0003261
- Occasional (5% to 29% of cases)
- Increased total eosinophil countHPOHP:0001880
- Occasional (5% to 29% of cases)
- Monoclonal elevation of circulating IgAHPOHP:0032335
- Occasional (5% to 29% of cases)
Where it sits
- A kind of