histiocytoma, Angiomatoid fibrous
Findings
No curated finding names histiocytoma, Angiomatoid fibrous yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A low malignant potential soft tissue neoplasm of uncertain differentiation. It typically affects young patients, presenting as a slowly growing nodular or cystic tumor mass, most often in the subcutaneous tissues of the extremities. Occasionally, patients have systemic symptoms (anemia, fever, and weight loss). This tumor has a relatively good prognosis. A minority of patients develop local recurrences. Metastases are rare.
Definition from the Mondo Disease Ontology (MONDO:0012809), read 2026-09-29. CC BY 4.0.
- Inheritance
- Typified by somatic mosaicism
HPO, annotations 2026-09-02
Features
1 feature
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- HistiocytomaHPOHP:0012315
Where it sits
- A kind of
Other names
4 names
Resolves to: histiocytoma, Angiomatoid fibrous
- Also called
- AFHangiomatoid fibrous histiocytomaangiomatoid malignant fibrous histiocytomahistiocytoma, angiomatoid fibrous, somatic