hilar cholangiocarcinoma
MONDO:0003345Mondo
Findings
No curated finding names hilar cholangiocarcinoma yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A cholangiocarcinoma that arises from the junction, or adjacent to the junction, of the right and left hepatic ducts.
Definition from the Mondo Disease Ontology (MONDO:0003345), read 2026-09-29. CC BY 4.0.
Features
10 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- CholangiocarcinomaHPOHP:0030153
- Very frequent (80% to 99% of cases)
- Extrahepatic cholestasisHPOHP:0012334
- Very frequent (80% to 99% of cases)
- JaundiceHPOHP:0000952
- Very frequent (80% to 99% of cases)
- HepatomegalyHPOHP:0002240
- Frequent (30% to 79% of cases)
- LymphadenopathyHPOHP:0002716
- Frequent (30% to 79% of cases)
- Abdominal painHPOHP:0002027
- Occasional (5% to 29% of cases)
- FatigueHPOHP:0012378
- Occasional (5% to 29% of cases)
- FeverHPOHP:0001945
- Occasional (5% to 29% of cases)
- Venous thrombosisHPOHP:0004936
- Occasional (5% to 29% of cases)
- Weight lossHPOHP:0001824
- Occasional (5% to 29% of cases)
Where it sits
- A kind of
Other names
6 names
Resolves to: hilar cholangiocarcinoma
- Also called
- cholangiocarcinoma of hilar portion of hepatic ducthilar CChilar CCAhilar portion of hepatic duct cholangiocarcinomaKlatskin tumorKlatskin's tumor