hereditary clear cell renal cell carcinoma
MONDO:0018492Mondo
Findings
No curated finding names hereditary clear cell renal cell carcinoma yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A manifestation of von Hippel-Lindau disease or other familial renal cell cancer syndromes that present as a malignant epithelial neoplasm of the kidney. It is characterized by the presence of lipid-containing clear cells within a vascular network. The tumor usually is bilateral and polycentric, and metastasizes to unusual sites. Late metastasis is common.
Definition from the Mondo Disease Ontology (MONDO:0018492), read 2026-09-29. CC BY 4.0.
Where it sits
Other names
4 names
Resolves to: hereditary clear cell renal cell carcinoma
- Also called
- hereditary clear cell renal carcinomahereditary clear cell renal cell adenocarcinomaHereditary clear cell renal cell cancerhereditary conventional (clear cell) renal cell carcinoma