hemihydranencephaly
MONDO:1040007Mondo
Findings
No curated finding names hemihydranencephaly yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A rare congenital brain disorder characterized by complete or almost near-complete unilateral absence of the cortical cortex, which is filled by a sac of cerebrospinal fluid. The presumed cause is a prenatal vascular disruption with occlusion of the carotid artery territories ipsilateral to the damaged brain.
Definition from the Mondo Disease Ontology (MONDO:1040007), read 2026-09-29. CC BY 4.0.
Where it sits
- A kind of
Other names
1 name
Resolves to: hemihydranencephaly
- Also called
- hemi-hydranencephaly