febrile ulceronecrotic Mucha-Habermann disease
Findings
No curated finding names febrile ulceronecrotic Mucha-Habermann disease yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a rare and severe form of pityriasis lichenoides et varioliformis acuta (PLEVA). PLEVA is characterized by skin lesions that ulcerate, breakdown, form open sores, then form a red-brown crust. FUMHD often begins as PLEVA, but then rapidly and suddenly progresses to large, destructive ulcers. There may be fever and extensive, painful loss of skin tissue as well as secondary infection of the ulcers. Diagnosis of FUMHD is confirmed by biopsy of skin lesions. FUMHD occurs more frequently in children, peaking at age 5 to 10. Males tend to be affected more often than females. While some cases of FUMHD have resolved without therapy, others have resulted in death. Early diagnosis and prompt treatment may help to reduce morbidity and death.
Definition from the Mondo Disease Ontology (MONDO:0023134), read 2026-09-29. CC BY 4.0.
Where it sits
- A kind of
Other names
1 name
Resolves to: febrile ulceronecrotic Mucha-Habermann disease
- Also called
- febrile ulceronecrotic pityriasis lichenoides acuta