extraskeletal myxoid chondrosarcoma
Findings
No curated finding names extraskeletal myxoid chondrosarcoma yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A rare malignant soft tissue neoplasm of uncertain differentiation, characterized by the presence of chondroblast-like cells in a myxoid stroma and a multinodular growth pattern. The most common sites of involvement are the deep soft tissues of the extremities, particularly the thigh. It usually presents as an enlarging soft tissue mass. Patients may have long survivals, but local recurrences and metastases occur in approximately half of the cases. The most common site of metastasis is the lungs.
Definition from the Mondo Disease Ontology (MONDO:0012825), read 2026-09-29. CC BY 4.0.
Where it sits
- Narrower terms (1)
Other names
4 names
Resolves to: extraskeletal myxoid chondrosarcoma
- Also called
- extraosseous chondrosarcomaextraskeletal chondrosarcomamyxoid extraosseous chondrosarcomamyxoid extraskeletal chondrosarcoma