extraskeletal Ewing sarcoma/peripheral primitive neuroectodermal tumor
Findings
No curated finding names extraskeletal Ewing sarcoma/peripheral primitive neuroectodermal tumor yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A spectrum of malignant tumors arising from the soft tissues, characterized morphologically by the presence of small round cells. Ewing sarcoma and peripheral primitive neuroectodermal tumor represent the ends of a spectrum, with Ewing sarcoma lacking evidence of neural differentiation and the markers that characterize the peripheral primitive neuroectodermal tumor. Ewing sarcoma and peripheral primitive neuroectodermal tumor may share cytogenetic abnormalities, proto-oncogene expression, cell culture and immunohistochemical abnormalities. Pain and the presence of a mass are the most common clinical symptoms.
Definition from the Mondo Disease Ontology (MONDO:0021039), read 2026-09-29. CC BY 4.0.
Where it sits
Other names
5 names
Resolves to: extraskeletal Ewing sarcoma/peripheral primitive neuroectodermal tumor
- Also called
- extraosseous Ewing sarcoma/peripheral primitive neuroectodermal tumorextraosseous Ewing sarcoma/peripheral primitive neuroectodermal tumourextraosseous Ewing's sarcoma/peripheral primitive neuroectodermal tumorextraosseous Ewing's sarcoma/peripheral primitive neuroectodermal tumourextraosseous Ewings sarcoma-primitive neuroepithelial tumor