extranodal nasal NK/T cell lymphoma
Findings
No curated finding names extranodal nasal NK/T cell lymphoma yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A rare, malignant neoplasm mainly affecting men in the fifth decade of life, that usually arises in the nose, paranasal sinuses, orbits or upper airway, and that can present with a nasal mass, nasal bleeding, nasal obstruction, palate perforation (i.e. midline perforation of the hard palate), and mid-facial and/or upper airway destructive lesions. In advanced disease stages, which are associated with a poor prognosis, NKTCL may disseminate to other organs. A few cases of NKTCL presenting primarily in the lymph nodes have also been described.
Definition from the Mondo Disease Ontology (MONDO:0019472), read 2026-09-29. CC BY 4.0.
Where it sits
Other names
9 names
Resolves to: extranodal nasal NK/T cell lymphoma
- Also called
- angiocentric T-cell lymphomaExtranodal NK/T lymphoma-nasalExtranodal NK/T-cell lymphoma, nasal typelethal midline granulomanasal T/natural killer-cell lymphomanasal type Extranodal NK/T-cell lymphomaNK/T-cell lymphomaNKTCLreticulosis, malignant