extraneural perineurioma
Findings
No curated finding names extraneural perineurioma yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Extraneural perineurioma is a rare tumor of cranial and spinal nerves arising from peripheral nerve sheet and composed exclusively or predominantly of cells showing perineurial differentiation. It presents as a well-circumscribed, rarely encapsulated mass, not associated with a recognizable nerve, most commonly arising in the dermis and subcutis of the extremities or trunk, or, rarely, in deep soft tissue or skin (e.g., in the stomach, kidney, pancreas, maxillary sinus, mandible, bronchial tree and the face). The clinical presentation depends on the localization.
Definition from the Mondo Disease Ontology (MONDO:0015031), read 2026-09-29. CC BY 4.0.
Where it sits
- A kind of
- Narrower terms (2)
Other names
1 name
Resolves to: extraneural perineurioma
- Also called
- soft tissue perineurioma