encircling double aortic arch
Findings
No curated finding names encircling double aortic arch yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Encircling double aortic arch is a very rare congenital anomaly of the great arteries characterized by the presence of two aortic arches (right and left) which encircle and compress the trachea and esophagus, resulting in various respiratory and gastrointestinal symptoms (e.g. harsh breathing, stridor, dyspnea, cyanotic and choking episodes, chronic cough, recurrent respiratory tract infections, dysphagia and reflux). Esophageal atresia and tracheoesophageal fistula have also been reported. It usually occurs isolated, but, on occasion, may be associated with other congenital heart anomalies and chromosomal aberations.
Definition from the Mondo Disease Ontology (MONDO:0020413), read 2026-09-29. CC BY 4.0.
Where it sits
- A kind of