ectopic aldosterone-producing tumor
Findings
No curated finding names ectopic aldosterone-producing tumor yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Ectopic aldosterone-producing tumor is an extremely rare aldosterone-producing neoplasm composed of aberrant adrenocortical tissue located outside the adrenal glands (e.g. in retroperitoneum, perirenal or periaortic fatty tissue, thorax, spinal canal, testes, ovaries) typically characterized by symptoms related to increased aldosterone levels (such as sustained, treatment-resistant hypertension and hypokalemia) or symptoms caused by local tumor enlargement.
Definition from the Mondo Disease Ontology (MONDO:0016506), read 2026-09-29. CC BY 4.0.
Features
12 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Decreased circulating renin concentrationHPOHP:0003351
- Obligate (100% of cases)
- Glucocortocoid-insensitive primary hyperaldosteronismHPOHP:0011740
- Obligate (100% of cases)
- HypertensionHPOHP:0000822
- Obligate (100% of cases)
- HeadacheHPOHP:0002315
- Very frequent (80% to 99% of cases)
- HypokalemiaHPOHP:0002900
- Very frequent (80% to 99% of cases)
- Ovarian neoplasmHPOHP:0100615
- Very frequent (80% to 99% of cases)
- Renal cortical adenoma
Where it sits
- A kind of
Other names
2 names
Resolves to: ectopic aldosterone-producing tumor
- Also called
- Extra-adrenal aldosterone-producing tumorExtra-adrenal aldosterone-producing tumour