double outlet left ventricle
MONDO:0018090Mondo
Findings
No curated finding names double outlet left ventricle yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Double-outlet left ventricle (DOLV) is an extremely rare congenital cardiac malformation in which both the aorta and the pulmonary artery arise, either exclusively or predominantly, from the morphologic left ventricle.
Definition from the Mondo Disease Ontology (MONDO:0018090), read 2026-09-29. CC BY 4.0.
Features
17 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Double outlet left ventricleHPOHP:0011581
- Obligate (100% of cases)
- Abnormal right ventricular functionHPOHP:0033118
- Very frequent (80% to 99% of cases)
- Patent ductus arteriosusHPOHP:0001643
- Very frequent (80% to 99% of cases)
- Ventricular septal defectHPOHP:0001629
- Very frequent (80% to 99% of cases)
- Abnormal coronary artery courseHPOHP:0011686
- Frequent (30% to 79% of cases)
- CardiomegalyHPOHP:0001640
- Frequent (30% to 79% of cases)
- CyanosisHPOHP:0000961
- Frequent (30% to 79% of cases)
- Tricuspid atresiaHPOHP:0011662
- Frequent (30% to 79% of cases)
- CryptorchidismHPOHP:0000028
- Occasional (5% to 29% of cases)
- Failure to thriveHPOHP:0001508
- Occasional (5% to 29% of cases)
- HypertelorismHPOHP:0000316
- Occasional (5% to 29% of cases)
- Orofacial cleftHPOHP:0000202
- Occasional (5% to 29% of cases)
Show the remaining 5
- Systolic heart murmurHPOHP:0031664
- Occasional (5% to 29% of cases)
- TachypneaHPOHP:0002789
- Occasional (5% to 29% of cases)
- Bicuspid pulmonary valveHPOHP:0005182
- Very rare (1% to 4% of cases)
- Pulmonary artery stenosisHPOHP:0004415
- Very rare (1% to 4% of cases)
- Pulmonary valve atresiaHPOHP:0010882
- Very rare (1% to 4% of cases)
Where it sits
- A kind of
Other names
2 names
Resolves to: double outlet left ventricle
- Also called
- DOLVdouble outlet left ventricle (disease)