desmoplastic infantile astrocytoma
MONDO:0022963Mondo
Findings
No curated finding names desmoplastic infantile astrocytoma yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A WHO grade I large cystic tumor that occurs almost exclusively in infants, with a prominent desmoplastic stroma having a neuroepithelial population consisting mainly of neoplastic astrocytes. It involves the superficial cerebral cortex and leptomeninges, and often attaches to the dura. Although clinically it presents as large tumor, it generally has a good prognosis following surgical resection. (Adapted from WHO)
Definition from the Mondo Disease Ontology (MONDO:0022963), read 2026-09-29. CC BY 4.0.
Where it sits
- A kind of
Other names
2 names
Resolves to: desmoplastic infantile astrocytoma
- Also called
- Desmoplastic astrocytoma of infancyDIA