dentin dysplasia-sclerotic bones syndrome
MONDO:0007438Mondo
Findings
No curated finding names dentin dysplasia-sclerotic bones syndrome yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A rare, genetic odontologic disease characterized by the clinical, radiographic, and histologic features of dentine dysplasia and osteosclerosis of all long bones, with heavy cortical bone and narrowed or occluded marrow spaces. There have been no further descriptions in the literature since 1977.
Definition from the Mondo Disease Ontology (MONDO:0007438), read 2026-09-29. CC BY 4.0.
Where it sits
- A kind of