congenital panfollicular nevus
Findings
No curated finding names congenital panfollicular nevus yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Congenital panfollicular nevus is a rare, benign, skin tumor disorder characterized by the presence of congenital, large (few centimeters), elevated, well-circumscribed, pink-tan, multinodular, non-ulcerative, bosselated-surface skin lesions located on the neck, scalp or hand and which enlarge with time. Histologically, hamartomatous proliferation containing irregularly arranged, malformed hair follicles in various stages of development, surrounded by fibrous tissue and densely distributed within the dermis is observed.
Definition from the Mondo Disease Ontology (MONDO:0015341), read 2026-09-29. CC BY 4.0.
Features
4 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- HamartomaHPOHP:0010566
- Obligate (100% of cases)
- Skin noduleHPOHP:0200036
- Very frequent (80% to 99% of cases)
- Verrucous papuleHPOHP:0012500
- Very frequent (80% to 99% of cases)
- HyperkeratosisHPOHP:0000962
- Frequent (30% to 79% of cases)
Reported absent (2)
- PainHPOHP:0012531
- PruritusHPOHP:0000989
Where it sits
- A kind of
Other names
1 name
Resolves to: congenital panfollicular nevus
- Also called
- congenital panfollicular nevus (disease)