clear cell sarcoma of kidney
MONDO:0005006Mondo
Findings
No curated finding names clear cell sarcoma of kidney yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A rare pediatric sarcoma affecting the kidney. It is characterized by the presence of epithelioid or spindle cells forming cords or nests, separated by fibrovascular septa. It is associated with internal tandem duplications in the BCOR gene. It metastasizes to lung, bone, brain and soft tissue.
Definition from the Mondo Disease Ontology (MONDO:0005006), read 2026-09-29. CC BY 4.0.
Where it sits
- A kind of
Other names
12 names
Resolves to: clear cell sarcoma of kidney
- Also called
- CCSKchildhood clear cell sarcoma of the kidneychildhood kidney clear cell sarcomachildhood renal clear cell sarcomaclear cell sarcoma - kidneyclear cell sarcoma of the kidneykidney clear cell sarcomapaediatric kidney clear cell sarcomapaediatric renal clear cell sarcomapediatric kidney clear cell sarcomapediatric renal clear cell sarcomarenal clear cell sarcoma