CD4+/CD56+ hematodermic neoplasm
MONDO:0019467Mondo
Findings
No curated finding names CD4+/CD56+ hematodermic neoplasm yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
An aggressive immature hematologic neoplasm formerly known as blastic NK cell lymphoma, composed of cells with a lymphoblast-like morphology. Recent evidence suggests derivation from a plasmacytoid monocyte. Patients present with cutaneous tumors and bone marrow involvement.
Definition from the Mondo Disease Ontology (MONDO:0019467), read 2026-09-29. CC BY 4.0.
Where it sits
Other names
11 names
Resolves to: CD4+/CD56+ hematodermic neoplasm
- Also called
- agranular CD4+ CD56+ hematodermic neoplasm/tumoragranular CD4+ natural Killer cell leukaemiaagranular CD4+ natural Killer cell leukemiablastic natural Killer leukemia/lymphomablastic NK-cell lymphomablastic plasmacytoid Dendritic cell neoplasmBPDCNearly plasmacytoid Dendritic cell leukemia/lymphomalymphoblastoid variant of NK-cell lymphomamonomorphic NK-cell lymphomaprimary cutaneous CD4+/CD56+ hematolymphoid neoplasm