behavioral variant of frontotemporal dementia
Findings
No curated finding names behavioral variant of frontotemporal dementia yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Behavioral variant of frontotemporal dementia (bv-FTD) is a form of frontotemporal dementia (FTD), characterized by progressive behavioral impairment and a decline in executive function with frontal lobe-predominant atrophy.
Definition from the Mondo Disease Ontology (MONDO:0017160), read 2026-09-29. CC BY 4.0.
Features
40 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Aggressive behaviorHPOHP:0000718
- Very frequent (80% to 99% of cases)
- AphasiaHPOHP:0002381
- Very frequent (80% to 99% of cases)
- Atypical behaviorHPOHP:0000708
- Very frequent (80% to 99% of cases)
- DisinhibitionHPOHP:0000734
- Very frequent (80% to 99% of cases)
- DyscalculiaHPOHP:0002442
- Very frequent (80% to 99% of cases)
- DysgraphiaHPOHP:0010526
- Very frequent (80% to 99% of cases)
- DyslexiaHPOHP:0010522
- Very frequent (80% to 99% of cases)
- EcholaliaHPOHP:0010529
- Very frequent (80% to 99% of cases)
- Emotional dearthHPOHP:0030213
- Very frequent (80% to 99% of cases)
- Frontotemporal cerebral atrophyHPOHP:0006892
- Very frequent (80% to 99% of cases)
- Frontotemporal dementiaHPOHP:0002145
- Very frequent (80% to 99% of cases)
- HyperoralityHPOHP:0000710
- Very frequent (80% to 99% of cases)
Show the remaining 28
- Inappropriate behaviorHPOHP:0000719
- Very frequent (80% to 99% of cases)
- IrritabilityHPOHP:0000737
- Very frequent (80% to 99% of cases)
- Lack of insightHPOHP:0000757
- Very frequent (80% to 99% of cases)
- Loss of speechHPOHP:0002371
- Very frequent (80% to 99% of cases)
- Memory impairmentHPOHP:0002354
- Very frequent (80% to 99% of cases)
- Mental deteriorationHPOHP:0001268
- Very frequent (80% to 99% of cases)
Genes
2 genes
Germline variants in the gene encoding each protein, as classified by GenCC submitters, each in their own words. Limited, disputed and refuted submissions are listed too.
Where it sits
Other names
1 name
Resolves to: behavioral variant of frontotemporal dementia
- Also called
- bv-FTD