atypical coarctation of aorta
Findings
No curated finding names atypical coarctation of aorta yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Middle aortic coarctation is a rare vascular anomaly characterized by the segmental narrowing of the abdominal and/or distal descending thoracic aorta with varying involvement of the visceral and renal arteries that commonly presents in children and young adults with early onset and refractory hypertension, abdominal angina, lower-limb claudication and that can lead to life-threatening complications associated with severe hypertension (i.e. myocardial infarction, heart failure, aortic rupture, renal insufficiency and intracranial hemorrhage). It may be due to various congenital or acquired causes, but it is most often secondary to an acquired inflammatory disease (i.e. Takayasu arteritis or giant cell arteritis).
Definition from the Mondo Disease Ontology (MONDO:0015446), read 2026-09-29. CC BY 4.0.
Where it sits
- A kind of
Other names
5 names
Resolves to: atypical coarctation of aorta
- Also called
- coarctation of the abdominal aortamid-aortic dysplastic syndromemid-aortic syndromeMidaortic syndromemiddle aortic syndrome