angiosarcoma
MONDO:0016982Mondo
Findings
No curated finding names angiosarcoma yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A malignant tumor arising from the endothelial cells of the blood vessels. Microscopically, it is characterized by frequently open vascular anastomosing and branching channels. The malignant cells that line the vascular channels are spindle or epithelioid and often display hyperchromatic nuclei. Angiosarcomas most frequently occur in the skin and breast. Patients with long-standing lymphedema are at increased risk of developing angiosarcoma.
Definition from the Mondo Disease Ontology (MONDO:0016982), read 2026-09-29. CC BY 4.0.
Where it sits
- A kind of
- Narrower terms (19)
- angiosarcoma of the scalp
- aorta angiosarcoma
- bone angiosarcoma
- breast angiosarcoma
- central nervous system angiosarcoma
- conventional angiosarcoma
- gallbladder angiosarcoma
- Kaposi's sarcoma
- liver angiosarcoma
- mediastinum angiosarcoma
- ovarian angiosarcoma
- pediatric angiosarcoma
- prostate angiosarcoma
- pulmonary artery leiomyosarcoma
- pulmonary vein leiomyosarcoma
- skin angiosarcoma
- spleen angiosarcoma
- superior vena cava angiosarcoma
- thyroid gland angiosarcoma
Other names
8 names
Resolves to: angiosarcoma
- Also called
- angiosarcoma (disease)blood vessel sarcomahemangiosarcomahemangiosarcoma, malignantmalignant angioendotheliomamalignant hemangioendotheliomasarcoma of blood vesselvascular sarcoma