amyopathic dermatomyositis
Findings
No curated finding names amyopathic dermatomyositis yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A form of dermatomyositis characterized by the presence of typical skin finding swithout muscle weakness. Some of the skin changes that suggest dermatomyositis include a pink rash on the face, neck, forearms and upper chest; Gottron's papules and heliotrope eyelids. Pruritis and photosensitivity are common, as is scalp inflammation and thinning of the hair.While patients with amyopathic dermatomyositis should not have clinically evident muscle weakness, minor muscle abnormalities may be included.Fatigue is reported in at least 50% of patients. Some cases have beenassociated with internal malignancy and/or interstitial lung disease. Treatment may include sun avoidance, ample use of sunscreen, topical corticosteroids, antimalarial agents, methotrexate, mycophenolate mofetil, or intravenous (IV) immunoglobulin.
Definition from the Mondo Disease Ontology (MONDO:0043317), read 2026-09-29. CC BY 4.0.
Where it sits
Other names
1 name
Resolves to: amyopathic dermatomyositis
- Also called
- dermatomyositis sine myositis