acute chest syndrome
MONDO:0005632Mondo
Findings
No curated finding names acute chest syndrome yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A vaso-occlusive crisis of the pulmonary vasculature occurring in patients with sickle cell disease. It is characterized by the presence of a new radiodensity on a chest radiograph accompanied by fever, cough, sputum production, dyspnea, or hypoxia.
Definition from the Mondo Disease Ontology (MONDO:0005632), read 2026-09-29. CC BY 4.0.
Features
2 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, hp/releases/2026-09-01.
- Increased total leukocyte countMondoHP:0001974
- TachypneaMondoHP:0002789
Where it sits
Other names
1 name
Resolves to: acute chest syndrome
- Also called
- ACS