acquired polycythemia vera
MONDO:0009891Mondo
Findings
No curated finding names acquired polycythemia vera yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Polycythemia vera (PV) is an acquired myeloproliferative disorder characterized by an elevated absolute red blood cell mass caused by uncontrolled red blood cell production, frequently associated with uncontrolled white blood cell and platelet production.
Definition from the Mondo Disease Ontology (MONDO:0009891), read 2026-09-29. CC BY 4.0.
- Inheritance
- Typified by somatic mosaicism
- Onset and course
- Late onset · Middle age onset · Intermediate young adult onset
HPO, annotations 2026-09-02
Features
37 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- SplenomegalyHPOHP:0001744
- 30 of 31 reported patients
- Very frequent (80% to 99% of cases)
- Abdominal painHPOHP:0002027
- Very frequent (80% to 99% of cases)
- Acute leukemiaHPOHP:0002488
- Very frequent (80% to 99% of cases)
- Angina pectorisHPOHP:0001681
- Very frequent (80% to 99% of cases)
- Bruising susceptibilityHPOHP:0000978
- Very frequent (80% to 99% of cases)
- EpistaxisHPOHP:0000421
- Very frequent (80% to 99% of cases)
Show the remaining 25
- PolycythemiaHPOHP:0001901
- Very frequent (80% to 99% of cases)
- TinnitusHPOHP:0000360
- Very frequent (80% to 99% of cases)
- VertigoHPOHP:0002321
- Very frequent (80% to 99% of cases)
- Weight lossHPOHP:0001824
- Very frequent (80% to 99% of cases)
- Abnormality of visionHPOHP:0000504
- Frequent (30% to 79% of cases)
- ArthralgiaHPOHP:0002829
- Frequent (30% to 79% of cases)
Where it sits
Other names
8 names
Resolves to: acquired polycythemia vera
- Also called
- acquired primary erythrocytosisOsler-Vaquez diseasepolycythaemia rubra verapolycythemia rubra verapolycythemia verapolycythemia vera, somaticPVVaquez disease